World Journal of Oncology, ISSN 1920-4531 print, 1920-454X online, Open Access
Article copyright, the authors; Journal compilation copyright, World J Oncol and Elmer Press Inc
Journal website https://www.wjon.org

Review

Volume 14, Number 1, February 2023, pages 15-20


Adult Primary Retroperitoneal Lymphangioma: Updated Facts

Figure

Figure 1.
Figure 1. An abdomino-pelvic CT scan (coronal plane) showing a large septated, multiloculated right retroperitoneal cystic mass, displacing the right colon medially. CT: computed tomography.

Tables

Table 1. Demographic Features and Clinical Presentation of Adult Patients With Primary ARL
 
ARL: adult retroperitoneal lymphangioma; F: female; M: male.
Age (years)
  Average45
  Range19 - 82
F/M ratio2.8:1
Clinical presentation
  Asymptomatic20%
  Symptomatic80%
Symptoms
  Abdominal pain62.5%
  Increased abdominal girth19%
  Self-palpable mass17.5%
  Nausea8.7%
  Vomiting3.7%
  Anorexia2.5%
  Back pain2.5%
  Food intolerance1.25%
  Flank pain1.25%
  Hematuria1.25%
  Cough1.25%
  Fatigue1.25%
  Constipation1.25%
  Fever1.25%

 

Table 2. Radiological Features Reported for 64 Patients With Primary ARL
 
Radiological characteristicsFrequency (%)
ARL: adult retroperitoneal lymphangioma.
Tumor features
  Unilocular17%
  Multilocular83%
Retroperitoneal location
  Right42%
  Mid20%
  Left38%
Combined
  Right multilocular cyst38%
  Mid multilocular cyst15%
  Left multilocular cyst30%
  Right unilocular cyst4%
  Mid unilocular cyst5%
  Left unilocular cyst8%